Persistent Hyperplastic Primary Vitreous

Source:http://linkedlifedata.com/resource/umls/id/C0266568

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MSH: A developmental ocular anomaly in which the primary VITREOUS BODY and its surrounding hyaloid vasculature failed to regress. It is usually unilateral and characterized by CATARACT; MICROPHTHALMOS (small eyeballs), and retrolenticular fibrovascular tissue. (from Yanoff: Ophthalmology, 2nd ed.)
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