Hemangioendothelioma, Epithelioid

Source:http://linkedlifedata.com/resource/umls/id/C0206732

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MSH: A tumor of medium-to-large veins, composed of plump-to-spindled endothelial cells that bulge into vascular spaces in a tombstone-like fashion. These tumors are thought to have "borderline" aggression, where one-third develop local recurrences, but only rarely metastasize. It is unclear whether the epithelioid hemangioendothelioma is truly neoplastic or an exuberant tissue reaction, nor is it clear if this is equivalent to Kimura's disease (see ANGIOLYMPHOID HYPERPLASIA WITH EOSINOPHILIA). (Segen, Dictionary of Modern Medicine, 1992),NCI: An angiocentric vascular tumor composed of epithelioid endothelial cells arranged in short cords and nests in a distinctive myxohyaline stroma. This tumor has metastatic potential.,NCI: A low grade malignant blood vessel neoplasm characterized by the presence of epithelioid endothelial cells, hylanized and myxoid stroma formation, and angiocentricity. It may present as a painful mass.
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