alveolar rhabdomyosarcoma

Source:http://linkedlifedata.com/resource/umls/id/C0206655

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MSH: A form of RHABDOMYOSARCOMA occurring mainly in adolescents and young adults, affecting muscles of the extremities, trunk, orbital region, etc. It is extremely malignant, metastasizing widely at an early stage. Few cures have been achieved and the prognosis is poor. "Alveolar" refers to its microscopic appearance simulating the cells of the respiratory alveolus. (Holland et al., Cancer Medicine, 3d ed, p2188),NCI: A soft tissue tumor that is most common in older children and teenagers. It begins in embryonic muscle cells (cells that develop into muscles in the body). It can occur at many places in the body, but usually occurs in the trunk, arms, or legs.,NCI: A primitive, malignant round cell neoplasm that cytologically resembles lymphoma and which shows partial skeletal muscle differentiation. Recurrent cytogenetic aberrations are specifically associated with this entity: t(2;13)(q35;q14) and t(1;13)(p36;q14).,NCI: A rapidly growing malignant mesenchymal neoplasm. It is characterized by the presence of r
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