mesenchymal chondrosarcoma

Source:http://linkedlifedata.com/resource/umls/id/C0206637

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MSH: A rare aggressive variant of chondrosarcoma, characterized by a biphasic histologic pattern of small compact cells intermixed with islands of cartilaginous matrix. Mesenchymal chondrosarcomas have a predilection for flat bones; long tubular bones are rarely affected. They tend to occur in the younger age group and are highly metastatic. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1456),NCI: A rare malignant tumor characterized by a bimorphic pattern composed of undifferentiated small round cells and islands of well differentiated hyaline cartilage.,NCI: A rare morphologic variant of chondrosarcoma. It is characterized by the presence of malignant small round cells, biphasic growth pattern, and well differentiated hyaline cartilage. Clinical presentation includes pain and swelling. The clinical course is aggressive, with local recurrences and distant metastases.
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