dentinogenesis imperfecta

Source:http://linkedlifedata.com/resource/umls/id/C0011436

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MSH: An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.,NCI: A congenital tooth development disorder caused by mutations in the DSPP gene. The teeth are weak, discolored, and translucent.
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