Switch to
| Predicate | Object |
|---|---|
| rdf:type | |
| lifeskim:mentions | |
| pubmed:issue |
6-7
|
| pubmed:dateCreated |
1997-1-2
|
| pubmed:abstractText |
Purtilo's syndrome or X-linked lymphoproliferative syndrome (XLP) is a rare genetic disorder affecting boys who have a selective immunodeficit towards Epstein Barr Virus (EBV) and who develop extremely severe forms of EBV infection, of which there are four major types: severe or fatal infectious mononucleosis (60 p. 100), lymphoma (23 p. 100), acquired hypo- or agamaglobulinemia (25 p. 100) and anemia or pancytopenia. We report a case of vasculitis (cutaneous and neurologic) which led to the discovery of a selective immunodeficit towards EBV, similar to Purtilo's syndrome.
|
| pubmed:language |
fre
|
| pubmed:journal | |
| pubmed:citationSubset |
IM
|
| pubmed:status |
MEDLINE
|
| pubmed:issn |
0151-9638
|
| pubmed:author | |
| pubmed:issnType |
Print
|
| pubmed:volume |
123
|
| pubmed:owner |
NLM
|
| pubmed:authorsComplete |
Y
|
| pubmed:pagination |
387-92
|
| pubmed:dateRevised |
2006-11-15
|
| pubmed:meshHeading |
pubmed-meshheading:8959062-Adolescent,
pubmed-meshheading:8959062-Herpesviridae Infections,
pubmed-meshheading:8959062-Herpesvirus 4, Human,
pubmed-meshheading:8959062-Humans,
pubmed-meshheading:8959062-Immunologic Deficiency Syndromes,
pubmed-meshheading:8959062-Male,
pubmed-meshheading:8959062-Skin Diseases, Vascular,
pubmed-meshheading:8959062-Syndrome,
pubmed-meshheading:8959062-Treatment Failure,
pubmed-meshheading:8959062-Vasculitis
|
| pubmed:year |
1996
|
| pubmed:articleTitle |
[Cutaneous and neurologic vasculitis disclosing EBV-selective immunodeficiency].
|
| pubmed:affiliation |
CHU de Nantes, Hötel-Dieu.
|
| pubmed:publicationType |
Journal Article,
English Abstract,
Case Reports
|