Statements in which the resource exists as a subject.
PredicateObject
rdf:type
lifeskim:mentions
pubmed:issue
4
pubmed:dateCreated
1983-11-23
pubmed:abstractText
Progress has been made in the diagnosis and management of the idiopathic long Q-T syndrome. The association of typical repolarization abnormalities and syncope during stress is characteristic of this syndrome. The pathogenetic mechanism has been largely, although not completely, elucidated. The data available support the hypothesis of a congenital imbalance between right and left-sided cardiac sympathetic innervation with left dominance; sudden sympathetic neural discharges trigger the malignant arrhythmias. Although mortality in untreated patients is extremely high, either beta-adrenergic blocking agents or a high thoracic left sympathectomy provide protection. Because many questions remain unanswered, a world-wide prospective registry has been initiated to provide the necessary information on the management of these patients. The registry constitutes a long-term (25 years) follow-up program and includes over 200 patients affected by the long Q-T syndrome.
pubmed:language
eng
pubmed:journal
pubmed:citationSubset
AIM
pubmed:chemical
pubmed:status
MEDLINE
pubmed:month
Oct
pubmed:issn
0003-4819
pubmed:author
pubmed:issnType
Print
pubmed:volume
99
pubmed:owner
NLM
pubmed:authorsComplete
Y
pubmed:pagination
561-2
pubmed:dateRevised
2007-11-15
pubmed:meshHeading
pubmed:year
1983
pubmed:articleTitle
The idiopathic long Q-T syndrome.
pubmed:publicationType
Journal Article