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pubmed-article:17577546pubmed:abstractTextA rare case of anaplastic ameloblastic fibrosarcoma (AS) arising in an ameloblastic fibroma (AF) of the maxilla of a 48-year-old patient 10 years after the primary excision is presented. The recurrent tumor retained focal areas of AF but manifested heterogeneous malignant features ranging from low-grade spindle to highly pleomorphic sarcomas. Biomarker analysis showed alterations of the p53 and c-KIT genes restricted to the sarcomatous component. The biological implications of these findings in the future management of these tumors are discussed.lld:pubmed
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pubmed-article:17577546pubmed:dateRevised2009-11-19lld:pubmed
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pubmed-article:17577546pubmed:articleTitleAnaplastic ameloblastic fibrosarcoma arising from recurrent ameloblastic fibroma: restricted molecular abnormalities of certain genes to the malignant transformation.lld:pubmed
pubmed-article:17577546pubmed:affiliationDepartment of Pathology, University of Texas M. D. Anderson Cancer Center, Houston, TX 77030, USA. anaggar@mdanderson.orglld:pubmed
pubmed-article:17577546pubmed:publicationTypeJournal Articlelld:pubmed
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