Source:http://linkedlifedata.com/resource/pubmed/id/17352108
Switch to
Predicate | Object |
---|---|
rdf:type | |
lifeskim:mentions | |
pubmed:issue |
4
|
pubmed:dateCreated |
2007-3-13
|
pubmed:abstractText |
Congenital portosystemic shunt (CEPS) is a rare condition that was first reported by John Abernethy in 1793. Two types of CEPS are described: type I (side to end anastomosis) or congenital absence of the portal vein, and type II (side to side anastomosis) with portal vein supply partially conserved. Type I CEPS is usually seen in girls and associates multiple malformations as polysplenia, malrotation, and cardiac anomalies. Type II is even rarer with no sex preference and no malformations associated. Hepatic encephalopathy is a common complication of both types in adulthood. Liver transplantation is the only effective treatment for symptomatic type I CEPS. A therapeutic approach for type II could be surgical closure of the shunt.
|
pubmed:language |
spa
|
pubmed:journal | |
pubmed:citationSubset |
IM
|
pubmed:status |
MEDLINE
|
pubmed:month |
Oct
|
pubmed:issn |
0214-1221
|
pubmed:author | |
pubmed:issnType |
Print
|
pubmed:volume |
19
|
pubmed:owner |
NLM
|
pubmed:authorsComplete |
Y
|
pubmed:pagination |
204-9
|
pubmed:meshHeading |
pubmed-meshheading:17352108-Arteriovenous Malformations,
pubmed-meshheading:17352108-Child, Preschool,
pubmed-meshheading:17352108-Female,
pubmed-meshheading:17352108-Humans,
pubmed-meshheading:17352108-Infant, Newborn,
pubmed-meshheading:17352108-Magnetic Resonance Imaging,
pubmed-meshheading:17352108-Male,
pubmed-meshheading:17352108-Portal System,
pubmed-meshheading:17352108-Syndrome
|
pubmed:year |
2006
|
pubmed:articleTitle |
[Congenital portosystemic shunt. The Abernethy malformation].
|
pubmed:affiliation |
Departamento de Cirugía Pediátrica, Hospital Infantil Universitario La Paz, Madrid. lfavila73@hotmail.com
|
pubmed:publicationType |
Journal Article,
English Abstract,
Case Reports
|