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pubmed-article:1694830pubmed:abstractTextWe describe 76 patients in whom a double inlet atrioventricular connexion was guarded by a common atrioventricular valve. The atriums were connected to a dominant right ventricle in 42, to a left ventricle in 29 and to a solitary indeterminate ventricle in 5. The most common atrial arrangement was isomerism of the right atrial appendages, seen in 46% (35/76). Of these, there was associated anomalous pulmonary venous connexion in 72% and absence of the spleen in 63%. Double outlet right ventricle was the most frequent ventriculoarterial connexion, present in 37 cases. Abnormal atrioventricular valvar function could already be detected in 46% of cases at the time of initial presentation. A decrease of function was observed in 18 patients, in 14 of them 2 weeks to 16 years (mean 5.7 years) after palliative surgery. The majority of the palliative procedures were constructions of shunts, since 75% (57/76) of the patients showed obstruction to flow of pulmonary blood. Patients with double inlet ventricle guarded by a common atrioventricular valve have a high early mortality (37% died in the neonatal period). Management should be designed to protect the integrity of the pulmonary vascular bed. Definitive repair with a Fontan type procedure is the most suitable final approach.lld:pubmed
pubmed-article:1694830pubmed:languageenglld:pubmed
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pubmed-article:1694830pubmed:authorpubmed-author:TruslerG AGAlld:pubmed
pubmed-article:1694830pubmed:authorpubmed-author:WilliamsW GWGlld:pubmed
pubmed-article:1694830pubmed:authorpubmed-author:FreedomR MRMlld:pubmed
pubmed-article:1694830pubmed:authorpubmed-author:SteinJ IJIlld:pubmed
pubmed-article:1694830pubmed:authorpubmed-author:ColesJ GJGlld:pubmed
pubmed-article:1694830pubmed:authorpubmed-author:SmallhornJ...lld:pubmed
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pubmed-article:1694830pubmed:volume28lld:pubmed
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pubmed-article:1694830pubmed:pagination7-17lld:pubmed
pubmed-article:1694830pubmed:dateRevised2006-11-15lld:pubmed
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pubmed-article:1694830pubmed:year1990lld:pubmed
pubmed-article:1694830pubmed:articleTitleCommon atrioventricular valve guarding double inlet atrioventricular connexion: natural history and surgical results in 76 cases.lld:pubmed
pubmed-article:1694830pubmed:affiliationDepartment of Pediatrics, University of Toronto, Faculty of Medicine, Ontario, Canada.lld:pubmed
pubmed-article:1694830pubmed:publicationTypeJournal Articlelld:pubmed
pubmed-article:1694830pubmed:publicationTypeResearch Support, Non-U.S. Gov'tlld:pubmed
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