pubmed-article:1694830 | rdf:type | pubmed:Citation | lld:pubmed |
pubmed-article:1694830 | lifeskim:mentions | umls-concept:C0543467 | lld:lifeskim |
pubmed-article:1694830 | lifeskim:mentions | umls-concept:C0542557 | lld:lifeskim |
pubmed-article:1694830 | lifeskim:mentions | umls-concept:C1274040 | lld:lifeskim |
pubmed-article:1694830 | lifeskim:mentions | umls-concept:C0175860 | lld:lifeskim |
pubmed-article:1694830 | lifeskim:mentions | umls-concept:C0205173 | lld:lifeskim |
pubmed-article:1694830 | lifeskim:mentions | umls-concept:C0868928 | lld:lifeskim |
pubmed-article:1694830 | pubmed:issue | 1 | lld:pubmed |
pubmed-article:1694830 | pubmed:dateCreated | 1990-8-13 | lld:pubmed |
pubmed-article:1694830 | pubmed:abstractText | We describe 76 patients in whom a double inlet atrioventricular connexion was guarded by a common atrioventricular valve. The atriums were connected to a dominant right ventricle in 42, to a left ventricle in 29 and to a solitary indeterminate ventricle in 5. The most common atrial arrangement was isomerism of the right atrial appendages, seen in 46% (35/76). Of these, there was associated anomalous pulmonary venous connexion in 72% and absence of the spleen in 63%. Double outlet right ventricle was the most frequent ventriculoarterial connexion, present in 37 cases. Abnormal atrioventricular valvar function could already be detected in 46% of cases at the time of initial presentation. A decrease of function was observed in 18 patients, in 14 of them 2 weeks to 16 years (mean 5.7 years) after palliative surgery. The majority of the palliative procedures were constructions of shunts, since 75% (57/76) of the patients showed obstruction to flow of pulmonary blood. Patients with double inlet ventricle guarded by a common atrioventricular valve have a high early mortality (37% died in the neonatal period). Management should be designed to protect the integrity of the pulmonary vascular bed. Definitive repair with a Fontan type procedure is the most suitable final approach. | lld:pubmed |
pubmed-article:1694830 | pubmed:language | eng | lld:pubmed |
pubmed-article:1694830 | pubmed:journal | http://linkedlifedata.com/r... | lld:pubmed |
pubmed-article:1694830 | pubmed:citationSubset | IM | lld:pubmed |
pubmed-article:1694830 | pubmed:status | MEDLINE | lld:pubmed |
pubmed-article:1694830 | pubmed:month | Jul | lld:pubmed |
pubmed-article:1694830 | pubmed:issn | 0167-5273 | lld:pubmed |
pubmed-article:1694830 | pubmed:author | pubmed-author:TruslerG AGA | lld:pubmed |
pubmed-article:1694830 | pubmed:author | pubmed-author:WilliamsW GWG | lld:pubmed |
pubmed-article:1694830 | pubmed:author | pubmed-author:FreedomR MRM | lld:pubmed |
pubmed-article:1694830 | pubmed:author | pubmed-author:SteinJ IJI | lld:pubmed |
pubmed-article:1694830 | pubmed:author | pubmed-author:ColesJ GJG | lld:pubmed |
pubmed-article:1694830 | pubmed:author | pubmed-author:SmallhornJ... | lld:pubmed |
pubmed-article:1694830 | pubmed:issnType | Print | lld:pubmed |
pubmed-article:1694830 | pubmed:volume | 28 | lld:pubmed |
pubmed-article:1694830 | pubmed:owner | NLM | lld:pubmed |
pubmed-article:1694830 | pubmed:authorsComplete | Y | lld:pubmed |
pubmed-article:1694830 | pubmed:pagination | 7-17 | lld:pubmed |
pubmed-article:1694830 | pubmed:dateRevised | 2006-11-15 | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:meshHeading | pubmed-meshheading:1694830-... | lld:pubmed |
pubmed-article:1694830 | pubmed:year | 1990 | lld:pubmed |
pubmed-article:1694830 | pubmed:articleTitle | Common atrioventricular valve guarding double inlet atrioventricular connexion: natural history and surgical results in 76 cases. | lld:pubmed |
pubmed-article:1694830 | pubmed:affiliation | Department of Pediatrics, University of Toronto, Faculty of Medicine, Ontario, Canada. | lld:pubmed |
pubmed-article:1694830 | pubmed:publicationType | Journal Article | lld:pubmed |
pubmed-article:1694830 | pubmed:publicationType | Research Support, Non-U.S. Gov't | lld:pubmed |
http://linkedlifedata.com/r... | pubmed:referesTo | pubmed-article:1694830 | lld:pubmed |