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Predicate | Object |
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rdf:type | |
lifeskim:mentions | |
pubmed:issue |
1
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pubmed:dateCreated |
1990-8-13
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pubmed:abstractText |
We describe 76 patients in whom a double inlet atrioventricular connexion was guarded by a common atrioventricular valve. The atriums were connected to a dominant right ventricle in 42, to a left ventricle in 29 and to a solitary indeterminate ventricle in 5. The most common atrial arrangement was isomerism of the right atrial appendages, seen in 46% (35/76). Of these, there was associated anomalous pulmonary venous connexion in 72% and absence of the spleen in 63%. Double outlet right ventricle was the most frequent ventriculoarterial connexion, present in 37 cases. Abnormal atrioventricular valvar function could already be detected in 46% of cases at the time of initial presentation. A decrease of function was observed in 18 patients, in 14 of them 2 weeks to 16 years (mean 5.7 years) after palliative surgery. The majority of the palliative procedures were constructions of shunts, since 75% (57/76) of the patients showed obstruction to flow of pulmonary blood. Patients with double inlet ventricle guarded by a common atrioventricular valve have a high early mortality (37% died in the neonatal period). Management should be designed to protect the integrity of the pulmonary vascular bed. Definitive repair with a Fontan type procedure is the most suitable final approach.
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pubmed:language |
eng
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pubmed:journal | |
pubmed:citationSubset |
IM
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pubmed:status |
MEDLINE
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pubmed:month |
Jul
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pubmed:issn |
0167-5273
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pubmed:author | |
pubmed:issnType |
Print
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pubmed:volume |
28
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
7-17
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pubmed:dateRevised |
2006-11-15
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pubmed:meshHeading |
pubmed-meshheading:1694830-Blood Vessel Prosthesis,
pubmed-meshheading:1694830-Child,
pubmed-meshheading:1694830-Double Outlet Right Ventricle,
pubmed-meshheading:1694830-Heart Atria,
pubmed-meshheading:1694830-Humans,
pubmed-meshheading:1694830-Mitral Valve,
pubmed-meshheading:1694830-Palliative Care,
pubmed-meshheading:1694830-Pulmonary Artery,
pubmed-meshheading:1694830-Spleen,
pubmed-meshheading:1694830-Tricuspid Valve
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pubmed:year |
1990
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pubmed:articleTitle |
Common atrioventricular valve guarding double inlet atrioventricular connexion: natural history and surgical results in 76 cases.
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pubmed:affiliation |
Department of Pediatrics, University of Toronto, Faculty of Medicine, Ontario, Canada.
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pubmed:publicationType |
Journal Article,
Research Support, Non-U.S. Gov't
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