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rdf:type |
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lifeskim:mentions |
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pubmed:issue |
1
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pubmed:dateCreated |
2006-1-18
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pubmed:abstractText |
We report a case of pantothenate kinase-associated neurodegeneration with increased regional cerebral blood flow (rCBF) in bilateral lentiform nuclei on technetium Tc-99m ethyl cysteinate dimer single-photon emission CT (ECD-SPECT). A 6-year-old boy presented with opisthotonus. T2*-weighted MR images revealed areas of marked hypointensity with a hyperintense focus in bilateral globus pallidus, creating the characteristic eye-of-the-tiger appearance. ECD-SPECT showed increased rCBF in bilateral lentiform nuclei.
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pubmed:commentsCorrections |
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pubmed:language |
eng
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pubmed:journal |
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pubmed:citationSubset |
IM
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pubmed:chemical |
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pubmed:status |
MEDLINE
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pubmed:month |
Jan
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pubmed:issn |
0195-6108
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pubmed:author |
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pubmed:issnType |
Print
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pubmed:volume |
27
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
212-3
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pubmed:dateRevised |
2008-2-14
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pubmed:meshHeading |
pubmed-meshheading:16418386-Brain,
pubmed-meshheading:16418386-Cerebrovascular Circulation,
pubmed-meshheading:16418386-Child,
pubmed-meshheading:16418386-Corpus Striatum,
pubmed-meshheading:16418386-Cysteine,
pubmed-meshheading:16418386-Humans,
pubmed-meshheading:16418386-Magnetic Resonance Imaging,
pubmed-meshheading:16418386-Male,
pubmed-meshheading:16418386-Mutation,
pubmed-meshheading:16418386-Nerve Degeneration,
pubmed-meshheading:16418386-Organotechnetium Compounds,
pubmed-meshheading:16418386-Pantothenate Kinase-Associated Neurodegeneration,
pubmed-meshheading:16418386-Phosphotransferases (Alcohol Group Acceptor),
pubmed-meshheading:16418386-Radiopharmaceuticals,
pubmed-meshheading:16418386-Tomography, Emission-Computed, Single-Photon
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pubmed:year |
2006
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pubmed:articleTitle |
Pantothenate kinase-associated neurodegeneration with increased lentiform nuclei cerebral blood flow.
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pubmed:affiliation |
Department of Nuclear Medicine, Cancer Institute Hospital, Tokyo, Japan.
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pubmed:publicationType |
Journal Article,
Case Reports
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