Statements in which the resource exists as a subject.
PredicateObject
rdf:type
lifeskim:mentions
pubmed:issue
11
pubmed:dateCreated
1998-11-19
pubmed:abstractText
The clinical and histological features of 39 cases of desmoplastic small round cell tumor (DSRCT) diagnosed at M.D. Anderson Cancer Center are presented. Thirty-two of the patients were men and seven were women ranging in age from 10 to 41 years (mean, 25 years). Twenty-five of the 35 patients for whom follow-up information was available died of widespread metastases 8 to 50 months (mean, 25.2 months) from the time of their diagnosis and the remaining 10 were alive with disease. With the exception of two cases that occurred in the liver and in the scrotum, respectively, all of the cases originated within the abdominal and/or pelvic peritoneum. Eight tumors also involved the retroperitoneum. Although the characteristic histologic pattern of "small, blue cells" embedded in a dense fibrous stroma was seen in most cases, about one third of the tumors exhibited a wide range of morphologic features. The recognition of these uncommon morphologic variants of DSRCT is of paramount importance to avoid a misdiagnosis because these tumors could potentially be confused with other neoplastic conditions.
pubmed:language
eng
pubmed:journal
pubmed:citationSubset
IM
pubmed:chemical
pubmed:status
MEDLINE
pubmed:month
Nov
pubmed:issn
0147-5185
pubmed:author
pubmed:issnType
Print
pubmed:volume
22
pubmed:owner
NLM
pubmed:authorsComplete
Y
pubmed:pagination
1303-13
pubmed:dateRevised
2004-11-17
pubmed:meshHeading
pubmed:year
1998
pubmed:articleTitle
Desmoplastic small round cell tumor: I: a histopathologic study of 39 cases with emphasis on unusual histological patterns.
pubmed:affiliation
The University of Texas M.D. Anderson Cancer Center, Houston 77056, USA.
pubmed:publicationType
Journal Article, Case Reports