rdf:type |
|
lifeskim:mentions |
|
pubmed:issue |
1
|
pubmed:dateCreated |
1997-5-13
|
pubmed:abstractText |
Polyglucosan body disease (PBD) is a progressive neurological disorder beginning in adult life and associated pathologically with widespread accumulation of polyglucosan bodies (PB) in neuronal and astrocytic processes. We report the unique clinicopathological findings in an early onset spinocerebellar syndrome associated with massive PB deposition.
|
pubmed:language |
eng
|
pubmed:journal |
|
pubmed:citationSubset |
IM
|
pubmed:chemical |
|
pubmed:status |
MEDLINE
|
pubmed:month |
Jan
|
pubmed:issn |
0001-6314
|
pubmed:author |
|
pubmed:issnType |
Print
|
pubmed:volume |
95
|
pubmed:owner |
NLM
|
pubmed:authorsComplete |
Y
|
pubmed:pagination |
60-4
|
pubmed:dateRevised |
2006-8-16
|
pubmed:meshHeading |
pubmed-meshheading:9048988-Age of Onset,
pubmed-meshheading:9048988-Astrocytes,
pubmed-meshheading:9048988-Atrophy,
pubmed-meshheading:9048988-Autopsy,
pubmed-meshheading:9048988-Brain,
pubmed-meshheading:9048988-Cerebellum,
pubmed-meshheading:9048988-Diagnosis, Differential,
pubmed-meshheading:9048988-Glucans,
pubmed-meshheading:9048988-Glycogen Storage Disease Type IV,
pubmed-meshheading:9048988-Humans,
pubmed-meshheading:9048988-Inclusion Bodies,
pubmed-meshheading:9048988-Infant,
pubmed-meshheading:9048988-Male,
pubmed-meshheading:9048988-Middle Aged,
pubmed-meshheading:9048988-Neurons,
pubmed-meshheading:9048988-Peripheral Nerves,
pubmed-meshheading:9048988-Peripheral Nervous System Diseases,
pubmed-meshheading:9048988-Spinal Cord,
pubmed-meshheading:9048988-Spinocerebellar Degenerations
|
pubmed:year |
1997
|
pubmed:articleTitle |
Childhood-onset spinocerebellar syndrome associated with massive polyglucosan body deposition.
|
pubmed:affiliation |
Department of Neurology, University of Connecticut School of Medicine, Farmington, USA.
|
pubmed:publicationType |
Journal Article,
Case Reports
|