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Predicate | Object |
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rdf:type | |
lifeskim:mentions | |
pubmed:issue |
9
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pubmed:dateCreated |
1979-2-21
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pubmed:abstractText |
Five children with polysplenia syndrome are described. Cardiac catheterization or postmortem examination revealed the following cardiac anomalies: interruption of the inferior vena cava with azygos (or hemiazygos) continuation to the left superior vena cava and a single atrium or a large atrial septal defect in all five children; a ventricular septal defect in three; and a primitive ventricle in one case. Other anomalies found were: central liver in all five; a right-sided stomach in three; and multiple small spleens and bilateral left, bilobed lungs--found on autopsy--in two of the children. In four of the five patients, whose ECG was available, a negative P wave was present in leads II, III and AVF. This leftward and superiorly directed P wave axis should suggest a diagnosis of polysplenia syndrome in an infant with congenital heart disease. The cardiac anomalies are surgically correctable; therefore, early recognition of this syndrome is of practical importance.
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pubmed:language |
eng
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pubmed:journal | |
pubmed:citationSubset |
IM
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pubmed:status |
MEDLINE
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pubmed:month |
Sep
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pubmed:issn |
0021-2180
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pubmed:author | |
pubmed:issnType |
Print
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pubmed:volume |
14
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
948-53
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pubmed:dateRevised |
2004-11-17
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pubmed:meshHeading |
pubmed-meshheading:721422-Abnormalities, Multiple,
pubmed-meshheading:721422-Child,
pubmed-meshheading:721422-Child, Preschool,
pubmed-meshheading:721422-Female,
pubmed-meshheading:721422-Heart Defects, Congenital,
pubmed-meshheading:721422-Humans,
pubmed-meshheading:721422-Infant,
pubmed-meshheading:721422-Infant, Newborn,
pubmed-meshheading:721422-Liver,
pubmed-meshheading:721422-Lung,
pubmed-meshheading:721422-Male,
pubmed-meshheading:721422-Spleen,
pubmed-meshheading:721422-Stomach,
pubmed-meshheading:721422-Syndrome
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pubmed:year |
1978
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pubmed:articleTitle |
Polysplenia syndrome. A study of five new cases.
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pubmed:publicationType |
Journal Article,
Case Reports
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