Statements in which the resource exists as a subject.
PredicateObject
rdf:type
lifeskim:mentions
pubmed:issue
4
pubmed:dateCreated
1983-6-10
pubmed:abstractText
A case of sclerosing leucoencephalopathy with membranocystic lesions of adipose tissue was reported. A 38-year-old Japanese housewife, whose parents were consanguineous, developed gradually neuropsychiatric symptoms characterized by euphoria, gait disturbance and urinary incontinence, followed by spastic tetraplegia with epileptic convulsions and died eight years later. Neuropathologically a form of sudanophilic leucodystrophy with a prominent fibrillary gliosis (dissociation glio-myelinique) associated with axonal spheroids and calcospherite depositions was revealed. A peculiar membranocystic lesion of adipose tissue was recognized not only in the bone marrow but also in other areas. However, no apparent bone pathology was observed except for a ring-like pleated lamellar structure. This case was thought to be classified as heterogeneous phenotype of membranous lipodystrophy (Nasu).
pubmed:language
eng
pubmed:journal
pubmed:citationSubset
IM
pubmed:chemical
pubmed:status
MEDLINE
pubmed:issn
0015-5721
pubmed:author
pubmed:issnType
Print
pubmed:volume
36
pubmed:owner
NLM
pubmed:authorsComplete
Y
pubmed:pagination
409-16
pubmed:dateRevised
2004-11-17
pubmed:meshHeading
pubmed:year
1982
pubmed:articleTitle
Sclerosing leucoencephalopathy with membranocystic lesions of adipose tissue: a contribution to the pathology of Nasu disease.
pubmed:publicationType
Journal Article, Case Reports