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| Predicate | Object |
|---|---|
| rdf:type | |
| lifeskim:mentions | |
| pubmed:issue |
10
|
| pubmed:dateCreated |
1977-11-30
|
| pubmed:abstractText |
An accumulation of fatty acids having chain lengths of C22 to C26 was demonstrated in the cholesterol ester fraction of white matter from two boys with adrenoleukodystrophy. A similar accumulation of very long chain fatty acids was also shown in gangliosides and cerebrosides. A disorder of the one-carbon degradation system responsible for the metabolism of some of the very long chain fatty acids may be the basic enzymatic defect in this condition.
|
| pubmed:language |
eng
|
| pubmed:journal | |
| pubmed:citationSubset |
IM
|
| pubmed:chemical | |
| pubmed:status |
MEDLINE
|
| pubmed:month |
Oct
|
| pubmed:issn |
0028-3878
|
| pubmed:author | |
| pubmed:issnType |
Print
|
| pubmed:volume |
27
|
| pubmed:owner |
NLM
|
| pubmed:authorsComplete |
Y
|
| pubmed:pagination |
928-32
|
| pubmed:dateRevised |
2006-11-15
|
| pubmed:meshHeading |
pubmed-meshheading:561905-Adrenal Gland Diseases,
pubmed-meshheading:561905-Brain,
pubmed-meshheading:561905-Brain Chemistry,
pubmed-meshheading:561905-Brain Diseases,
pubmed-meshheading:561905-Child,
pubmed-meshheading:561905-Cholesterol Esters,
pubmed-meshheading:561905-Fatty Acids,
pubmed-meshheading:561905-Gangliosides,
pubmed-meshheading:561905-Humans,
pubmed-meshheading:561905-Male
|
| pubmed:year |
1977
|
| pubmed:articleTitle |
Adrenoleukodystrophy. Accumulation of cholesterol esters with very long chain fatty acids.
|
| pubmed:publicationType |
Journal Article,
Research Support, U.S. Gov't, P.H.S.,
Case Reports
|