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Predicate | Object |
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rdf:type | |
lifeskim:mentions | |
pubmed:issue |
6
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pubmed:dateCreated |
1989-2-17
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pubmed:abstractText |
Carney's triad is a rare syndrome characterized by gastric leiomyosarcoma, functioning extra-adrenal paraganglioma, and pulmonary chondroma. Twenty-seven cases are reported in literature: the most commonly observed neoplasm is gastric leiomyosarcoma (26/27) followed by lung tumor (22/27), and gastric paraganglioma (15/27). Three patients bearing a gastric leiomyosarcoma developed liver metastases, and 6 had a local recurrence after some years. The occurrence of paraganglioma makes the prognosis worse: 4 deaths from local infiltration, metastases or severe hypertension. The triad only occurred in 9/27 cases, mostly young female patients. A common embryologic origin is difficult to assess. The case of a young female patient with recurrent gastric leiomyosarcoma (12 years later) and bilateral pulmonary chondroma is described. It is important that patients with any of the three tumors be periodically examined.
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pubmed:language |
ita
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pubmed:journal | |
pubmed:citationSubset |
IM
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pubmed:status |
MEDLINE
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pubmed:month |
Dec
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pubmed:issn |
0033-8362
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pubmed:author | |
pubmed:issnType |
Print
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pubmed:volume |
76
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
577-9
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pubmed:dateRevised |
2008-10-21
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pubmed:meshHeading |
pubmed-meshheading:2850598-Child,
pubmed-meshheading:2850598-Chondroma,
pubmed-meshheading:2850598-Female,
pubmed-meshheading:2850598-Humans,
pubmed-meshheading:2850598-Leiomyosarcoma,
pubmed-meshheading:2850598-Lung Neoplasms,
pubmed-meshheading:2850598-Paraganglioma, Extra-Adrenal,
pubmed-meshheading:2850598-Stomach Neoplasms,
pubmed-meshheading:2850598-Syndrome
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pubmed:year |
1988
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pubmed:articleTitle |
[Carney's triad. Apropos of a case of recurrent gastric leiomyosarcoma and bilateral pulmonary chondroma].
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pubmed:affiliation |
U.O. di Radiodiagnostica dell'USSL, Università, Pisa.
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pubmed:publicationType |
Journal Article,
English Abstract,
Review,
Case Reports
|