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Predicate | Object |
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rdf:type | |
lifeskim:mentions | |
pubmed:issue |
2
|
pubmed:dateCreated |
1988-7-29
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pubmed:abstractText |
A 12-week-old girl presented with cutaneous haemangiomata and hemihypertrophy of the chest and right upper extremity--stigmata of the Klippel-Trenaunay-Weber syndrome. Screening cranial CT-scan followed by cerebral angiogram revealed what is believed to be the first reported occurrence of a cerebral arteriovenous fistula in a patient with this syndrome. Craniotomy and clip application successfully obliterated the fistula. Although rare at present, neurovascular involvement in the Klippel-Trenaunay-Weber syndrome may be found more frequently with the newer non-invasive diagnostic methods for screening these children. Such findings may strengthen the putative classification of this syndrome within the group of primary mesodermal (vascular) phakomatoses.
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pubmed:language |
eng
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pubmed:journal | |
pubmed:citationSubset |
IM
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pubmed:status |
MEDLINE
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pubmed:month |
Apr
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pubmed:issn |
0012-1622
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pubmed:author | |
pubmed:issnType |
Print
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pubmed:volume |
30
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
245-8
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pubmed:dateRevised |
2009-11-11
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pubmed:meshHeading |
pubmed-meshheading:2838360-Angiomatosis,
pubmed-meshheading:2838360-Cerebral Angiography,
pubmed-meshheading:2838360-Female,
pubmed-meshheading:2838360-Humans,
pubmed-meshheading:2838360-Infant,
pubmed-meshheading:2838360-Intracranial Arteriovenous Malformations,
pubmed-meshheading:2838360-Klippel-Trenaunay-Weber Syndrome,
pubmed-meshheading:2838360-Tomography, X-Ray Computed
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pubmed:year |
1988
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pubmed:articleTitle |
Cerebral arteriovenous fistula in the Klippel-Trenaunay-Weber syndrome.
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pubmed:affiliation |
Department of Surgery, University of Connecticut.
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pubmed:publicationType |
Journal Article,
Case Reports
|