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rdf:type |
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lifeskim:mentions |
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pubmed:issue |
5
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pubmed:dateCreated |
2010-11-5
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pubmed:abstractText |
Immune dysregulation, polyendocrinopathy, enteropathy, X-linked (IPEX) syndrome is characterized by severe systemic autoimmunity caused by mutations in the forkhead box protein 3 (FOXP3) gene. Hematopoietic cell transplantation is currently the only viable option for long-term survival, but patients are frequently very ill and may not tolerate traditional myeloablative conditioning regimens.
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pubmed:grant |
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pubmed:language |
eng
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pubmed:journal |
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pubmed:citationSubset |
AIM
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pubmed:chemical |
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pubmed:status |
MEDLINE
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pubmed:month |
Nov
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pubmed:issn |
1097-6825
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pubmed:author |
pubmed-author:BurroughsLauri MLM,
pubmed-author:CarpenterPaul APA,
pubmed-author:EnglundJanetJ,
pubmed-author:OchsHans DHD,
pubmed-author:RawlingsDavid JDJ,
pubmed-author:SandersJeanJ,
pubmed-author:ScharenbergAndrew MAM,
pubmed-author:Skoda-SmithSuzanneS,
pubmed-author:StorbRainerR,
pubmed-author:TorgersonTroy RTR,
pubmed-author:WoolfreyAnn EAE
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pubmed:copyrightInfo |
Copyright © 2010 American Academy of Allergy, Asthma & Immunology. Published by Mosby, Inc. All rights reserved.
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pubmed:issnType |
Electronic
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pubmed:volume |
126
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
1000-5
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pubmed:dateRevised |
2011-11-1
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pubmed:meshHeading |
pubmed-meshheading:20643476-Adolescent,
pubmed-meshheading:20643476-Cell Separation,
pubmed-meshheading:20643476-Child,
pubmed-meshheading:20643476-Cyclosporine,
pubmed-meshheading:20643476-Flow Cytometry,
pubmed-meshheading:20643476-Forkhead Transcription Factors,
pubmed-meshheading:20643476-Genetic Diseases, X-Linked,
pubmed-meshheading:20643476-Graft vs Host Disease,
pubmed-meshheading:20643476-Hematopoietic Stem Cell Transplantation,
pubmed-meshheading:20643476-Humans,
pubmed-meshheading:20643476-Immunologic Deficiency Syndromes,
pubmed-meshheading:20643476-Immunosuppressive Agents,
pubmed-meshheading:20643476-Infant,
pubmed-meshheading:20643476-Male,
pubmed-meshheading:20643476-Mycophenolic Acid,
pubmed-meshheading:20643476-Myeloablative Agonists,
pubmed-meshheading:20643476-Reverse Transcriptase Polymerase Chain Reaction,
pubmed-meshheading:20643476-Syndrome,
pubmed-meshheading:20643476-Transplantation Conditioning,
pubmed-meshheading:20643476-Vidarabine,
pubmed-meshheading:20643476-Whole-Body Irradiation
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pubmed:year |
2010
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pubmed:articleTitle |
Stable hematopoietic cell engraftment after low-intensity nonmyeloablative conditioning in patients with immune dysregulation, polyendocrinopathy, enteropathy, X-linked syndrome.
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pubmed:affiliation |
Fred Hutchinson Cancer Research Center, Seattle, Wash 98109-1024, USA. burroug@fhcrc.org
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pubmed:publicationType |
Journal Article,
Case Reports,
Research Support, Non-U.S. Gov't,
Research Support, N.I.H., Extramural
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