Statements in which the resource exists as a subject.
PredicateObject
rdf:type
lifeskim:mentions
pubmed:issue
4
pubmed:dateCreated
2009-10-2
pubmed:abstractText
Macrocephaly-cutis marmorata telangiectatica congenita is a rare overgrowth syndrome commonly associated with hydrocephalus. Although the pathophysiological characteristics of the hydrocephalus in this syndrome is not fully known, previous reports have described its treatment with ventriculoperitoneal shunt placement. The authors describe 2 cases of macrocephaly-cutis marmorata telangiectatica congenita successfully treated for progressive hydrocephalus with endoscopic third ventriculostomy. Both patients experienced clinical and radiographic stabilization following treatment, and these findings offer insight into the pathophysiology of the hydrocephalus and its ideal management.
pubmed:language
eng
pubmed:journal
pubmed:citationSubset
IM
pubmed:status
MEDLINE
pubmed:month
Oct
pubmed:issn
1933-0715
pubmed:author
pubmed:issnType
Electronic
pubmed:volume
4
pubmed:owner
NLM
pubmed:authorsComplete
Y
pubmed:pagination
397-401
pubmed:meshHeading
pubmed-meshheading:19795974-Abnormalities, Multiple, pubmed-meshheading:19795974-Cephalometry, pubmed-meshheading:19795974-Cerebellum, pubmed-meshheading:19795974-Disease Progression, pubmed-meshheading:19795974-Encephalocele, pubmed-meshheading:19795974-Female, pubmed-meshheading:19795974-Humans, pubmed-meshheading:19795974-Hydrocephalus, pubmed-meshheading:19795974-Infant, pubmed-meshheading:19795974-Magnetic Resonance Angiography, pubmed-meshheading:19795974-Magnetic Resonance Imaging, pubmed-meshheading:19795974-Magnetic Resonance Imaging, Cine, pubmed-meshheading:19795974-Male, pubmed-meshheading:19795974-Syndrome, pubmed-meshheading:19795974-Telangiectasis, pubmed-meshheading:19795974-Third Ventricle, pubmed-meshheading:19795974-Tomography, X-Ray Computed, pubmed-meshheading:19795974-Ventriculostomy
pubmed:year
2009
pubmed:articleTitle
Endoscopic third ventriculostomy to treat hydrocephalus associated with macrocephaly-cutis marmorata telangiectatica congenita.
pubmed:affiliation
Department of Clinical Neurosciences, Alberta Children's Hospital, University of Calgary, Alberta, Canada.
pubmed:publicationType
Journal Article, Case Reports