Linked Life Data

15704038

Source:http://linkedlifedata.com/resource/pubmed/id/15704038

Statements in which the resource exists as a subject.
PredicateObject
rdf:type
lifeskim:mentions
pubmed:dateCreated
2005-2-10
pubmed:abstractText
Marfan syndrome is a connective tissue disease with typical clinical signs and cardiac involvement. Its appearance in the neonatal period has a bad prognosis due to incompetence of all cardiac valves with subsequent congestive heart failure. Conservative management usually fails, the children die during their first year of life. We report on a girl with neonatal Marfan syndrome who suffered from regurgitance of all cardiac valves, enlarged ventricles, and dilated great arteries. She was NYHA class IV. At the age of six months she underwent heart transplantation. To prevent aneurysm formation and dissection of the great vessels, the whole aortic arch and pulmonary trunk were replaced as well.
pubmed:language
eng
pubmed:journal
pubmed:citationSubset
IM
pubmed:status
MEDLINE
pubmed:month
Feb
pubmed:issn
0171-6425
pubmed:author
pubmed:issnType
Print
pubmed:volume
53 Suppl 2
pubmed:owner
NLM
pubmed:authorsComplete
Y
pubmed:pagination
S146-8
pubmed:dateRevised
2007-11-15
pubmed:meshHeading
pubmed:year
2005
pubmed:articleTitle
Cardiac transplantation in neonatal Marfan syndrome -- a life-saving approach.
pubmed:affiliation
Department of Pediatric Cardiology, University Children's Hospital Münster, Münster, Germany. kraseman@uni-muenster.de
pubmed:publicationType
Journal Article, Case Reports