Source:http://linkedlifedata.com/resource/pubmed/id/15014899
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Predicate | Object |
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rdf:type | |
lifeskim:mentions | |
pubmed:issue |
9
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pubmed:dateCreated |
2004-9-27
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pubmed:abstractText |
The development of a diffuse elastic tissue defect resembling pseudoxanthoma elasticum (PXE) is a recently established and frequently encountered clinical entity in beta-thalassemia. The clinical spectrum of this disorder is not yet completely understood as it is continuously being enriched with novel complications that are often serious. We present here a thalassemia intermedia patient with typical PXE manifestations and a fusiform aneurysmatic dilatation of the ascending thoracic aorta, a previously unknown complication in these patients. An aortic aneurysm has itself a notable morbidity, while it may also impair the particularly susceptible cardiac function of beta-thalassemia patients, hence affecting the overall prognosis of the main disease.
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pubmed:language |
eng
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pubmed:journal | |
pubmed:citationSubset |
IM
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pubmed:status |
MEDLINE
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pubmed:month |
Sep
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pubmed:issn |
0939-5555
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pubmed:author | |
pubmed:issnType |
Print
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pubmed:volume |
83
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
596-9
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pubmed:dateRevised |
2004-11-17
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pubmed:meshHeading |
pubmed-meshheading:15014899-Adult,
pubmed-meshheading:15014899-Aorta,
pubmed-meshheading:15014899-Dilatation, Pathologic,
pubmed-meshheading:15014899-Female,
pubmed-meshheading:15014899-Humans,
pubmed-meshheading:15014899-Pseudoxanthoma Elasticum,
pubmed-meshheading:15014899-Syndrome,
pubmed-meshheading:15014899-Tomography, Emission-Computed,
pubmed-meshheading:15014899-beta-Thalassemia
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pubmed:year |
2004
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pubmed:articleTitle |
Aneurysmatic dilatation of ascending aorta in a patient with beta-thalassemia and a pseudoxanthoma elasticum-like syndrome.
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pubmed:affiliation |
First Department of Internal Medicine, University of Athens, Medical School, Laiko General Hospital, Athens, Greece. dfarm1@panafonet.gr
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pubmed:publicationType |
Journal Article,
Case Reports
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