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pubmed-article:12975426pubmed:abstractTextTo evaluate the acute haemodynamic effect of BQ-123, a selective endothelin A receptor antagonist, in severe chronic pulmonary arterial hypertension (PAH) of primary or autoimmune origin or related to congenital heart disease.lld:pubmed
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pubmed-article:12975426pubmed:articleTitleAcute endothelin A receptor antagonism improves pulmonary and systemic haemodynamics in patients with pulmonary arterial hypertension that is primary or autoimmune and related to congenital heart disease.lld:pubmed
pubmed-article:12975426pubmed:affiliationDepartment of Paediatric Cardiology, Onassis Cardiac Surgery Centre, Athens, Greece. riapos@hol.grlld:pubmed
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