Total colonic aganglionosis with ileal involvement is estimated at 1 case in 50,000 living births. This pathology has a very variable prognosis, and patients often need long-term parenteral nutrition. The aim of this study is to define prognostic factors for this disease.
Services de chirurgie Viscérale, de Gastro-entérologie, de Santé Publique, d'anesthésie, d'Anatomopathologie, de Génétique, Hôpital Robert Debre, Paris, France.
