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rdf:type |
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lifeskim:mentions |
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pubmed:issue |
4
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pubmed:dateCreated |
2001-11-26
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pubmed:abstractText |
A hereditary and an acquired type of C1-esterase inhibitor deficiency have been described. Manifestations characteristic of both forms include recurrent subcutaneous and submucosal angiooedema. Acquired C1-esterase inhibitor deficiency has been observed in association with lymphoproliferative disorders, malignancy, autoimmune diseases and infections. We report on a case with the acquired form of the disease accompanied by leucocytoclastic vasculitis. Treatment with antimalarial agents resulted in complete resolution of symptoms and signs. Furthermore, C1-esterase inhibitor concentration and activity, as well as C1 levels, all returned to normal.
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pubmed:language |
eng
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pubmed:journal |
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pubmed:citationSubset |
IM
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pubmed:chemical |
|
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pubmed:status |
MEDLINE
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pubmed:issn |
0001-5555
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pubmed:author |
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pubmed:issnType |
Print
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pubmed:volume |
81
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pubmed:owner |
NLM
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pubmed:authorsComplete |
Y
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pubmed:pagination |
298-300
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pubmed:dateRevised |
2009-11-19
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pubmed:meshHeading |
pubmed-meshheading:11720182-Adult,
pubmed-meshheading:11720182-Angioedema,
pubmed-meshheading:11720182-Antimalarials,
pubmed-meshheading:11720182-Chloroquine,
pubmed-meshheading:11720182-Complement C1 Inactivator Proteins,
pubmed-meshheading:11720182-Complement System Proteins,
pubmed-meshheading:11720182-Female,
pubmed-meshheading:11720182-Humans,
pubmed-meshheading:11720182-Hydroxychloroquine,
pubmed-meshheading:11720182-Treatment Outcome,
pubmed-meshheading:11720182-Vasculitis, Leukocytoclastic, Cutaneous
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|
pubmed:articleTitle |
Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis.
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pubmed:affiliation |
Allergology and Angioedema Outpatient Clinic, Semmelweis University, Kútvölgyi Centre, Budapest, Hungary. farkash@kut.sote.hu
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pubmed:publicationType |
Journal Article,
Case Reports,
Research Support, Non-U.S. Gov't
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