| umls-concept:C0206656 | skos:definition | MSH: A form of RHABDOMYOSARCOMA arising primarily in the head and neck, especially the orbit, of children below the age of 10. The cells are smaller than those of other rhabdomyosarcomas and are of two basic cell types: spindle cells and round cells. This cancer is highly sensitive to chemotherapy and has a high cure rate with multi-modality therapy. (From Holland et al., Cancer Medicine, 3d ed, p2188),NCI: A soft tissue tumor that is most common in infants and young children. It begins in muscles, usually in the head, neck, or genitourinary tract.,NCI: A primitive malignant soft tissue sarcoma that recapitulates the phenotypic and biological features of embryonic skeletal muscle. The term embryonal rhabdomyosarcoma encompasses the spindle cell, botryoid and anaplastic variants.,NCI: A poorly circumscribed morphologic variant of rhabdomyosarcoma. It is characterized by the presence of primitive skeletal muscle differentiation in any stage of myogenesis. There are three histologic types, spindle cell, botryoid | lld:umls |
