| umls-concept:C0205944 | skos:definition | NCI: A sarcoma of unknown lineage with predominantly epithelioid cytomorphology and predominantly affecting adolescents and young adults.,NCI: An aggressive malignant neoplasm of uncertain lineage, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma). | lld:umls |
