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umls-concept:C0034069 | skos:definition | MSH: A process in which normal lung tissues are progressively replaced by FIBROBLASTS and COLLAGEN causing an irreversible loss of the ability to transfer oxygen into the bloodstream via PULMONARY ALVEOLI. Patients show progressive DYSPNEA finally resulting in death.,MEDLINEPLUS: <p>Pulmonary fibrosis harms the tissues deep in your lungs. The air sacs in your lungs and their supporting structures become scarred and make your lungs thick and stiff. That makes it hard for you to catch your breath, and your blood may not get enough oxygen.</p><p>One cause of pulmonary fibrosis is <a href='http://www.nlm.nih.gov/medlineplus/interstitiallungdiseases.html'>interstitial lung disease</a>. Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. Pulmonary fibrosis is also associated with some connective tissue diseases. It can be a side effect of a medicine. Sometimes no one knows the cause of the disease. Smoking can boost your risk or make your illness worse</p>,NCI: A diso | lld:umls |
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