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pubmed-article:6255119pubmed:abstractTextThe association of neutropenia with type IB glycogen storage disease was observed in siblings. Biochemical studies of liver demonstrated a defect in glucose-6-phosphate transport. Neutrophil mobilization in vivo was impaired but the bone marrow was normal histologically. In vitro studies of neutrophils indicated a defect in random and directed cell migration. The studies suggest that a role for glucose-6-phosphate transport in neutrophils should be considered.lld:pubmed
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pubmed-article:6255119pubmed:articleTitleNeutropenia and impaired neutrophil migration in type IB glycogen storage disease.lld:pubmed
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