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pubmed-article:3072750pubmed:abstractTextTo determine the spectrum of urologic disease and the value of ultrasound as a screening mechanism, renal imaging was performed on 23 patients with Bardet-Biedl syndrome. On intravenous urography (IVU), abnormal calices were present in 22 patients, with communicating cortical cysts/diverticula in 17. Ultrasound detected caliceal or cystic changes in 70%. On IVU, 21 patients had fetal-type lobular outlines that were detected on sonography in 95%. Renal structural abnormalities are characteristic of the Bardet-Biedl syndrome, and are still best imaged by urography.lld:pubmed
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pubmed-article:3072750pubmed:articleTitleSonographic and urographic correlation in Bardet-Biedl syndrome (formerly Laurence-Moon-Biedl syndrome).lld:pubmed
pubmed-article:3072750pubmed:affiliationDepartment of Radiology, Memorial University, St. John's, Newfoundland, Canada.lld:pubmed
pubmed-article:3072750pubmed:publicationTypeJournal Articlelld:pubmed
pubmed-article:3072750pubmed:publicationTypeResearch Support, Non-U.S. Gov'tlld:pubmed
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