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pubmed-article:21195947pubmed:abstractTexthereditary angioedema (HAE) is a rare disorder characterized by a quantitative or functional deficiency of C1 esterase inhibitor (C1-INH), resulting in periodic attacks of acute edema at various body locations. The symptoms of these painful attacks can be treated effectively with C1-INH concentrate.lld:pubmed
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pubmed-article:21195947pubmed:articleTitleProspective study of C1 esterase inhibitor in the treatment of successive acute abdominal and facial hereditary angioedema attacks.lld:pubmed
pubmed-article:21195947pubmed:affiliationDallasAllergyImmunology, Dallas, Texas 75230, USA. richwasserman_pdai@yahoo.comlld:pubmed
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