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pubmed-article:20103510pubmed:dateCreated2010-3-25lld:pubmed
pubmed-article:20103510pubmed:abstractTextTo determine whether conventional coarctation repair results in sustained growth of hypoplastic transverse arches, we examined the follow-up of 20 patients operated through a thoracotomy between 1990 and 1995 who had available serial echocardiographic examinations. Mean age at operation was 8.6+/-5.7 days. In the distal transverse arch, maximum change was observed in the early postoperative period and sustained growth was observed thereafter. At last follow-up, no patients had Z-scores of less than -2. In contrast, only minimal growth occurred in the proximal transverse arch (mean Z-score diameter before and after repair: -1.87+/-0.12 vs. -1.66+/-0.09; P=0.05) in the postoperative period. At last follow-up, seven patients (35%) kept a diameter Z-score of less than -2, and 5 of them had a gradient of 15 mmHg (P=0.01). No correlation was found between the size of the proximal arch at last follow-up and its size before repair or technique used. CONCLUSION: Patients with moderately hypoplastic arch treated by conventional coarctation repair have adequate growth of the distal arch demonstrated at long-term follow-up, but one-third of them keep a small proximal arch. This subset of patients is at risk of developing hypertension and may warrant further investigation.lld:pubmed
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pubmed-article:20103510pubmed:authorpubmed-author:LiuJessie Y...lld:pubmed
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pubmed-article:20103510pubmed:volume10lld:pubmed
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pubmed-article:20103510pubmed:pagination582-6lld:pubmed
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pubmed-article:20103510pubmed:year2010lld:pubmed
pubmed-article:20103510pubmed:articleTitleModerately hypoplastic arches: do they reliably grow into adulthood after conventional coarctation repair?lld:pubmed
pubmed-article:20103510pubmed:affiliationDepartment of Cardiac Surgery, Royal Children's Hospital, University of Melbourne and the Murdoch Children's Research Institute, Melbourne, Australia.lld:pubmed
pubmed-article:20103510pubmed:publicationTypeJournal Articlelld:pubmed