A 36-year-old female with hemoglobin Nottingham (betaFG 5(98) Val --> Gly) causing severe hemolytic anemia and chronic thromboembolic pulmonary hypertension presented with symptomatic subacute right lower lobar pulmonary arterial thrombosis requiring surgical pulmonary thrombectomy. We describe a successful, multidisciplinary approach to the problems associated with this disease, particularly with the use of cardiopulmonary bypass and deep hypothermic circulatory arrest.
Department of Anesthesiology, Perioperative and Pain Medicine, Division of Cardiac Anesthesiology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA 02115, USA.
