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pubmed-article:17126138pubmed:abstractTextAbsent pulmonary valve syndrome (APVS) is a relatively rare anomaly that is usually associated with a ventricular septal defect and a restrictive pulmonary annulus with severe pulmonary regurgitation. The to-and-fro flow across the right ventricular outflow tract produces enormously dilated and pulsatile pulmonary arteries (PAs) that cause severe respiratory distress and tracheomalacia by compression of the trachea and primary bronchi. This retrospective study summarizes our 20-year experience of surgical treatment in patients with APVS.lld:pubmed
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pubmed-article:17126138pubmed:authorpubmed-author:BrownJohn WJWlld:pubmed
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pubmed-article:17126138pubmed:year2006lld:pubmed
pubmed-article:17126138pubmed:articleTitleSurgical treatment of absent pulmonary valve syndrome associated with bronchial obstruction.lld:pubmed
pubmed-article:17126138pubmed:affiliationSection of Cardiothoracic Surgery, Indiana University School of Medicine, Indianapolis, Indiana 46202-5123, USA. jobrown@iupui.edulld:pubmed
pubmed-article:17126138pubmed:publicationTypeJournal Articlelld:pubmed