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pubmed-article:12234951pubmed:abstractTextPrimary pulmonary hypertension (PPH) is a severe and progressive disease. Without treatment, the median survival is 2.8 years, with survival rates of 68%, 48%, and 34% at 1, 3, and 5 years, respectively. Intravenous epoprostenol was the first Food and Drug Administration-approved therapy for PPH. The long-term impact that epoprostenol has made on PPH remains to be defined.lld:pubmed
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pubmed-article:12234951pubmed:articleTitleSurvival in primary pulmonary hypertension: the impact of epoprostenol therapy.lld:pubmed
pubmed-article:12234951pubmed:affiliationRush-Presbyterian-St Luke's Medical Center, Department of Medicine, Section of Cardiology, Chicago, Ill 60612, USA. vmclaugh@rush.edulld:pubmed
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