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pubmed-article:7446557pubmed:abstractTextCardiac involvement in hemochromatosis typically results in congestive cardiomyopathy; a restrictive cardiomyopathy due to hemochromatosis is distinctly rare. A restrictive cardiomyopathy, which developed in the patient described in this report, was due to hemochromatosis which mimicked constrictive pericarditis clinically, echocardiographically and hemodynamically, and resulted in a thoracotomy for attempted surgical therapy. The fact that hemochromatosis represents the only cause of a restrictive cardiomyopathy that is potentially reversible by medical therapy makes early recognition of hemochromatosis heart disease important.lld:pubmed
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pubmed-article:7446557pubmed:articleTitleHemochromatosis heart disease: an unemphasized cause of potentially reversible restrictive cardiomyopathy.lld:pubmed
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