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pubmed-article:21255870pubmed:abstractTextIncontinentia pigmenti (IP) is a multisystem disorder, in which cutaneous symptoms can be accompanied by dental, ocular, and central nervous system defects. In adults, the clinical diagnosis of IP is based principally on the late onset of stage 4 lesions and their association with dental, nail, ocular, or central nervous system anomalies. Nevertheless, these lesions are often unrecognized.lld:pubmed
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pubmed-article:21255870pubmed:copyrightInfoCopyright © 2010 American Academy of Dermatology, Inc. Published by Mosby, Inc. All rights reserved.lld:pubmed
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pubmed-article:21255870pubmed:articleTitleClinical and histologic features of incontinentia pigmenti in adults with nuclear factor-?B essential modulator gene mutations.lld:pubmed
pubmed-article:21255870pubmed:affiliationCentre National de Référence des Maladies Génétiques à Expression Cutanée and the Department of Dermatology, Unité de Formation et de Recherche Necker-Enfants Malades Hospital, Université Paris V, Paris, France.lld:pubmed
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