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pubmed-article:20838339pubmed:abstractTextThoracic aortic aneurysm (TAA) dissection is an important cause of death in the western world. Especially in young adults, the genetic contribution to this disease is estimated to be high, as at least one out of five probands has a positive family history for aortic aneurysms/dissections. In recent years, major progress has been made in the identification of several genes underlying both syndromic and nonsyndromic forms of TAA.lld:pubmed
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pubmed-article:20838339pubmed:articleTitleThe Loeys-Dietz syndrome: an update for the clinician.lld:pubmed
pubmed-article:20838339pubmed:affiliationDepartment of Pediatrics, Ghent University Hospital, Ghent University, Ghent, Belgium.lld:pubmed
pubmed-article:20838339pubmed:publicationTypeJournal Articlelld:pubmed
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