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pubmed-article:20492031pubmed:abstractTextLoeys-Dietz syndrome (LDS) is a recently described connective tissue disorder characterized by generalized arterial tortuosity and aggressive aortopathy that untreated leads to early death even at aortic dimensions as small as 4 cm. We report the case of a young man with LDS successfully treated for aortic root, arch, and thoracoabdominal pathology.lld:pubmed
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pubmed-article:20492031pubmed:articleTitleTwo-stage total aortic replacement for Loeys-Dietz syndrome.lld:pubmed
pubmed-article:20492031pubmed:affiliationDivision of Thoracic and Cardiovascular Surgery, Department of Surgery, Duke University, Durham, North Carolina 27710, USA.lld:pubmed
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