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pubmed-article:19922436pubmed:abstractTextThrombotic thrombocytopenic purpura (TTP) is a rare, acute, life-threatening disorder, associated with a deficiency in ADAMTS 13. The majority of acute, idiopathic, adult TTP cases are associated with anti-ADAMTS 13 IgG antibodies. However, the factor(s) precipitating an acute TTP episode are not always obvious; indeed, a multifactorial etiology is likely.lld:pubmed
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pubmed-article:19922436pubmed:articleTitleHuman leukocyte antigen association in idiopathic thrombotic thrombocytopenic purpura: evidence for an immunogenetic link.lld:pubmed
pubmed-article:19922436pubmed:affiliationDepartment of Haematology, University College of London Hospitals, and Haemostasis Research Unit, University College London, London, UK. m.scully@ucl.ac.uklld:pubmed
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