| pubmed-article:19755920 | rdf:type | pubmed:Citation | lld:pubmed |
| pubmed-article:19755920 | lifeskim:mentions | umls-concept:C0087111 | lld:lifeskim |
| pubmed-article:19755920 | lifeskim:mentions | umls-concept:C0231335 | lld:lifeskim |
| pubmed-article:19755920 | lifeskim:mentions | umls-concept:C0878675 | lld:lifeskim |
| pubmed-article:19755920 | lifeskim:mentions | umls-concept:C0011900 | lld:lifeskim |
| pubmed-article:19755920 | pubmed:issue | 10 | lld:pubmed |
| pubmed-article:19755920 | pubmed:dateCreated | 2010-1-6 | lld:pubmed |
| pubmed-article:19755920 | pubmed:abstractText | Erdheim-Chester disease is a rare, non-Langerhans systemic histiocytosis characterized by bilateral sclerosis of the metaphyseal regions of the long bones and infiltration in other organs. The histopathologic hallmark is defined by a mononuclear infiltrate of foamy histiocytes and rare pathognomonic Touton giant cells with extensive fibrosis. This condition is exceptional in children. We report here a case of Erdheim-Chester disease in a 10-year-old girl with retroperitoneal infiltration and bone involvement, for whom the diagnosis was only established after a 3-year course with multiple biopsies. It is also the first pediatric case successfully treated with interferon-alpha suggesting that interferon-alpha can be a safe and efficient first-line therapy for this disease in children. | lld:pubmed |
| pubmed-article:19755920 | pubmed:language | eng | lld:pubmed |
| pubmed-article:19755920 | pubmed:journal | http://linkedlifedata.com/r... | lld:pubmed |
| pubmed-article:19755920 | pubmed:citationSubset | IM | lld:pubmed |
| pubmed-article:19755920 | pubmed:chemical | http://linkedlifedata.com/r... | lld:pubmed |
| pubmed-article:19755920 | pubmed:status | MEDLINE | lld:pubmed |
| pubmed-article:19755920 | pubmed:month | Oct | lld:pubmed |
| pubmed-article:19755920 | pubmed:issn | 1536-3678 | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:FabreMoniqueM | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:CharlotteFred... | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:HarocheJulien... | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:EidPierreP | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:TaoufikYassin... | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:Kone-PautIsab... | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:ParienteDanie... | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:DurrbachAntoi... | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:TranTu-AnhTA | lld:pubmed |
| pubmed-article:19755920 | pubmed:author | pubmed-author:CraiuIrinaI | lld:pubmed |
| pubmed-article:19755920 | pubmed:issnType | Electronic | lld:pubmed |
| pubmed-article:19755920 | pubmed:volume | 31 | lld:pubmed |
| pubmed-article:19755920 | pubmed:owner | NLM | lld:pubmed |
| pubmed-article:19755920 | pubmed:authorsComplete | Y | lld:pubmed |
| pubmed-article:19755920 | pubmed:pagination | 782-6 | lld:pubmed |
| pubmed-article:19755920 | pubmed:dateRevised | 2011-10-6 | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:meshHeading | pubmed-meshheading:19755920... | lld:pubmed |
| pubmed-article:19755920 | pubmed:year | 2009 | lld:pubmed |
| pubmed-article:19755920 | pubmed:articleTitle | Erdheim-Chester disease in childhood: a challenging diagnosis and treatment. | lld:pubmed |
| pubmed-article:19755920 | pubmed:affiliation | Department of Pediatrics, Pediatric Rheumatology, Bicêtre University Hospital, Le Kremlin Bicêtre, France. tu-anh.tran@bct.aphp.fr | lld:pubmed |
| pubmed-article:19755920 | pubmed:publicationType | Journal Article | lld:pubmed |
| pubmed-article:19755920 | pubmed:publicationType | Case Reports | lld:pubmed |
