pubmed-article:19158945 | rdf:type | pubmed:Citation | lld:pubmed |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0016719 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C1417701 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0242606 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0149784 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0040715 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0521447 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0221099 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C1522702 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0599718 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0599813 | lld:lifeskim |
pubmed-article:19158945 | lifeskim:mentions | umls-concept:C0599893 | lld:lifeskim |
pubmed-article:19158945 | pubmed:issue | 1 | lld:pubmed |
pubmed-article:19158945 | pubmed:dateCreated | 2009-1-22 | lld:pubmed |
pubmed-article:19158945 | pubmed:abstractText | Friedreich ataxia originates from a decrease in mitochondrial frataxin, which causes the death of a subset of neurons. The biochemical hallmarks of the disease include low activity of the iron sulfur cluster-containing proteins (ISP) and impairment of antioxidant defense mechanisms that may play a major role in disease progression. | lld:pubmed |
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pubmed-article:19158945 | pubmed:language | eng | lld:pubmed |
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pubmed-article:19158945 | pubmed:citationSubset | IM | lld:pubmed |
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pubmed-article:19158945 | pubmed:status | MEDLINE | lld:pubmed |
pubmed-article:19158945 | pubmed:issn | 1932-6203 | lld:pubmed |
pubmed-article:19158945 | pubmed:author | pubmed-author:HolmgrenArneA | lld:pubmed |
pubmed-article:19158945 | pubmed:author | pubmed-author:RustinPierreP | lld:pubmed |
pubmed-article:19158945 | pubmed:author | pubmed-author:AuchèreFranço... | lld:pubmed |
pubmed-article:19158945 | pubmed:author | pubmed-author:PaupeVincentV | lld:pubmed |
pubmed-article:19158945 | pubmed:author | pubmed-author:DassaEmmanuel... | lld:pubmed |
pubmed-article:19158945 | pubmed:author | pubmed-author:GoncalvesSerg... | lld:pubmed |
pubmed-article:19158945 | pubmed:author | pubmed-author:LönnMariaM | lld:pubmed |
pubmed-article:19158945 | pubmed:issnType | Electronic | lld:pubmed |
pubmed-article:19158945 | pubmed:volume | 4 | lld:pubmed |
pubmed-article:19158945 | pubmed:owner | NLM | lld:pubmed |
pubmed-article:19158945 | pubmed:authorsComplete | Y | lld:pubmed |
pubmed-article:19158945 | pubmed:pagination | e4253 | lld:pubmed |
pubmed-article:19158945 | pubmed:dateRevised | 2009-11-18 | lld:pubmed |
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