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pubmed-article:16995576pubmed:dateCreated2006-9-25lld:pubmed
pubmed-article:16995576pubmed:abstractTextFibrocalculous pancreatopathy (FCPP) is a secondary form of diabetes mellitus (DM) with obscure etiology. Recently various gene mutations have been reported in patients with FCPP from the Indian subcontinent. Initially termed tropical pancreatic diabetes, FCPP is uncommon and is characterized by pancreatic calcifications. The diagnosis is made in the third decade of life in most patients with the onset of abdominal pain and DM. We report a female child with DM diagnosed at the age of 3 years who had been managed with insulin but was ketosis resistant. The diagnosis of FCPP was made 3 years later. There were no mutations at N34S and P55S in the SPINK1 gene.lld:pubmed
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pubmed-article:16995576pubmed:year2006lld:pubmed
pubmed-article:16995576pubmed:articleTitleJuvenile fibrocalculous pancreatopathy--a patient report.lld:pubmed
pubmed-article:16995576pubmed:affiliationDepartment of Endocrinology, Sher-i-Kashmir Institute of Medical Sciences, Srinagar, Kashmir.lld:pubmed
pubmed-article:16995576pubmed:publicationTypeJournal Articlelld:pubmed
pubmed-article:16995576pubmed:publicationTypeCase Reportslld:pubmed