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pubmed-article:16984702pubmed:abstractTextWe report the first case, to the best of our knowledge, of a child with the unusual association of Moya-Moya disease and both systemic and pulmonary hypertension. Histological examination revealed fibromuscular dysplasia as the common denominator for a diffuse arteriopathy.lld:pubmed
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pubmed-article:16984702pubmed:articleTitleFibromuscular dysplasia as the substrate for systemic and pulmonary hypertension in the setting of Moya-Moya disease.lld:pubmed
pubmed-article:16984702pubmed:affiliationCardiologie Pédiatrique, Hôpital Necker-Enfants Malades, AP-HP, Paris, France. phalla.ou@nck.ap-hop-paris.frlld:pubmed
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