pubmed-article:16625352 | rdf:type | pubmed:Citation | lld:pubmed |
pubmed-article:16625352 | lifeskim:mentions | umls-concept:C0019621 | lld:lifeskim |
pubmed-article:16625352 | lifeskim:mentions | umls-concept:C0024485 | lld:lifeskim |
pubmed-article:16625352 | lifeskim:mentions | umls-concept:C2348519 | lld:lifeskim |
pubmed-article:16625352 | pubmed:issue | 9 | lld:pubmed |
pubmed-article:16625352 | pubmed:dateCreated | 2006-8-9 | lld:pubmed |
pubmed-article:16625352 | pubmed:abstractText | CNS complications of LCH include "space occupying" lesions corresponding to histiocytic granulomas and "neurodegenerative" presentation (ND-LCH) characterized by a progressive cerebellar ataxia. Studies analyzing specifically the MRI presentation of ND-LCH are scarce. We present here the MRIs of 13 patients registered as isolated ND-LCH. Posterior fossa was involved in 12 patients (92%), showing a symmetrical T2 hyperintensity of the cerebellar white matter areas in seven cases with a circumscribed T1 hyperintensity of the dentate nuclei in five cases, definite hyperintense T2 areas in the adjacent pontine tegmentum white matter in nine cases associated with a hyperintensity of the pontine pyramidal tracts in four cases. A cerebellar atrophy was noted in eight cases. The supratentorial region was involved in 11 patients, showing T2 hyperintense lesions in the cerebral white matter in eight cases and a discrete symmetrical T1 hyperintense signal in the globus pallidus in eight patients. A diffuse cortical atrophy was present in three cases and a marked focal atrophy of the corpus callosum in three cases. This series allows us to establish a not previously reported evocative semeiologic MR presentation to precisely orientate to the diagnosis of the pure neurodegenerative form of LCH. | lld:pubmed |
pubmed-article:16625352 | pubmed:language | eng | lld:pubmed |
pubmed-article:16625352 | pubmed:journal | http://linkedlifedata.com/r... | lld:pubmed |
pubmed-article:16625352 | pubmed:citationSubset | IM | lld:pubmed |
pubmed-article:16625352 | pubmed:status | MEDLINE | lld:pubmed |
pubmed-article:16625352 | pubmed:month | Sep | lld:pubmed |
pubmed-article:16625352 | pubmed:issn | 0938-7994 | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:ChirasJJ | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:Hoang-XuanKK | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:DonadieuJJ | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:GenereauTT | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:Martin-Duvern... | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:GuillevinRR | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:IdbaihAA | lld:pubmed |
pubmed-article:16625352 | pubmed:author | pubmed-author:French... | lld:pubmed |
pubmed-article:16625352 | pubmed:issnType | Print | lld:pubmed |
pubmed-article:16625352 | pubmed:volume | 16 | lld:pubmed |
pubmed-article:16625352 | pubmed:owner | NLM | lld:pubmed |
pubmed-article:16625352 | pubmed:authorsComplete | Y | lld:pubmed |
pubmed-article:16625352 | pubmed:pagination | 2074-82 | lld:pubmed |
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pubmed-article:16625352 | pubmed:year | 2006 | lld:pubmed |
pubmed-article:16625352 | pubmed:articleTitle | MRI features of neurodegenerative Langerhans cell histiocytosis. | lld:pubmed |
pubmed-article:16625352 | pubmed:affiliation | Department of Neuroradiology, GH Pitié-Salpêtrière, 47 Bd de l'Hôpital, 75013, Paris, France. nadine.martin-duverneuil@psl.ap-hop-paris.fr | lld:pubmed |
pubmed-article:16625352 | pubmed:publicationType | Journal Article | lld:pubmed |