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pubmed-article:16014041pubmed:abstractTextDent's disease, an X-linked renal tubular disorder, is characterized by low-molecular-weight proteinuria, hypercalciuria, nephrocalcinosis, nephrolithiasis, and progressive renal failure. Dent's disease results from mutations of the voltage-gated chloride channel CLC-5.lld:pubmed
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pubmed-article:16014041pubmed:articleTitleHigh citrate diet delays progression of renal insufficiency in the ClC-5 knockout mouse model of Dent's disease.lld:pubmed
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