pubmed-article:12203143 | rdf:type | pubmed:Citation | lld:pubmed |
pubmed-article:12203143 | lifeskim:mentions | umls-concept:C0005961 | lld:lifeskim |
pubmed-article:12203143 | lifeskim:mentions | umls-concept:C0272170 | lld:lifeskim |
pubmed-article:12203143 | pubmed:issue | 4 | lld:pubmed |
pubmed-article:12203143 | pubmed:dateCreated | 2002-8-30 | lld:pubmed |
pubmed-article:12203143 | pubmed:abstractText | Shwachman-Diamond syndrome is a rare autosomal recessive disorder characterized by exocrine pancreatic dysfunction, metaphyseal dysostosis and bone marrow dysfunction with a predilection towards severe hematologic complications. Allogeneic bone marrow transplantation has been used as a therapeutic approach for SDS patients with serious hematologic abnormalities with mixed results. There is some concern that these patients may be more susceptible to early (<100 days) transplant-related complications than other transplant groups. We report a patient who received a matched allogeneic transplant without developing serious early transplant-related complications, but eventually died from relapse of his disease. Although experience is limited, a review of the reported cases suggests patients with SDS may be transplanted without significant short-term morbidity and mortality. | lld:pubmed |
pubmed-article:12203143 | pubmed:language | eng | lld:pubmed |
pubmed-article:12203143 | pubmed:journal | http://linkedlifedata.com/r... | lld:pubmed |
pubmed-article:12203143 | pubmed:citationSubset | IM | lld:pubmed |
pubmed-article:12203143 | pubmed:status | MEDLINE | lld:pubmed |
pubmed-article:12203143 | pubmed:month | Aug | lld:pubmed |
pubmed-article:12203143 | pubmed:issn | 0268-3369 | lld:pubmed |
pubmed-article:12203143 | pubmed:author | pubmed-author:JonesR JRJ | lld:pubmed |
pubmed-article:12203143 | pubmed:author | pubmed-author:VogelsangGG | lld:pubmed |
pubmed-article:12203143 | pubmed:author | pubmed-author:BrodskyR ARA | lld:pubmed |
pubmed-article:12203143 | pubmed:author | pubmed-author:OrtP JPJ | lld:pubmed |
pubmed-article:12203143 | pubmed:issnType | Print | lld:pubmed |
pubmed-article:12203143 | pubmed:volume | 30 | lld:pubmed |
pubmed-article:12203143 | pubmed:owner | NLM | lld:pubmed |
pubmed-article:12203143 | pubmed:authorsComplete | Y | lld:pubmed |
pubmed-article:12203143 | pubmed:pagination | 255-8 | lld:pubmed |
pubmed-article:12203143 | pubmed:dateRevised | 2006-11-15 | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:meshHeading | pubmed-meshheading:12203143... | lld:pubmed |
pubmed-article:12203143 | pubmed:year | 2002 | lld:pubmed |
pubmed-article:12203143 | pubmed:articleTitle | Bone marrow transplantation in Shwachman-Diamond syndrome. | lld:pubmed |
pubmed-article:12203143 | pubmed:affiliation | Sidney Kimmel Comprehensive Cancer Center at Johns Hopkins, Baltimore, MD 21231, USA. | lld:pubmed |
pubmed-article:12203143 | pubmed:publicationType | Journal Article | lld:pubmed |
pubmed-article:12203143 | pubmed:publicationType | Review | lld:pubmed |
pubmed-article:12203143 | pubmed:publicationType | Case Reports | lld:pubmed |
pubmed-article:12203143 | pubmed:publicationType | Research Support, Non-U.S. Gov't | lld:pubmed |
http://linkedlifedata.com/r... | pubmed:referesTo | pubmed-article:12203143 | lld:pubmed |
http://linkedlifedata.com/r... | pubmed:referesTo | pubmed-article:12203143 | lld:pubmed |