pubmed-article:12142780 | rdf:type | pubmed:Citation | lld:pubmed |
pubmed-article:12142780 | lifeskim:mentions | umls-concept:C0684224 | lld:lifeskim |
pubmed-article:12142780 | lifeskim:mentions | umls-concept:C0927232 | lld:lifeskim |
pubmed-article:12142780 | lifeskim:mentions | umls-concept:C1266184 | lld:lifeskim |
pubmed-article:12142780 | lifeskim:mentions | umls-concept:C0242262 | lld:lifeskim |
pubmed-article:12142780 | pubmed:issue | 5 | lld:pubmed |
pubmed-article:12142780 | pubmed:dateCreated | 2002-7-26 | lld:pubmed |
pubmed-article:12142780 | pubmed:abstractText | Childhood atypical teratoid/rhabdoid tumor (AT/RT) of the central nervous system (CNS) is a recently described entity. Diagnosis is based on distinctive light microscopy and immunohistochemical findings, coupled with molecular genetic analysis. Most AT/RTs demonstrate monosomy 22 or deletions of chromosome band 22q11 with alterations of the hSNF5/INI1 gene. The tumor's incidence is still undefined, but it may comprise as high as 1 in 4 primitive CNS tumors in infants. Treatment is far from optimal, but there are occasional long-term survivors, especially among older children. Therapeutic approached have included surgery, chemotherapy, and radiotherapy. Prospective clinical trials are needed for children with AT/RTs. | lld:pubmed |
pubmed-article:12142780 | pubmed:language | eng | lld:pubmed |
pubmed-article:12142780 | pubmed:journal | http://linkedlifedata.com/r... | lld:pubmed |
pubmed-article:12142780 | pubmed:citationSubset | IM | lld:pubmed |
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pubmed-article:12142780 | pubmed:status | MEDLINE | lld:pubmed |
pubmed-article:12142780 | pubmed:issn | 1077-4114 | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:BiegelJaclyn... | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:PackerRoger... | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:SmithMalcolmM | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:FinlayJonatha... | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:BlaneySusanS | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:RorkeLucy BLB | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:VezinaGilbert... | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:KunLarryL | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:GeyerJ... | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:HeidemanRicha... | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:HildenJoanneJ | lld:pubmed |
pubmed-article:12142780 | pubmed:author | pubmed-author:JanssAnna JAJ | lld:pubmed |
pubmed-article:12142780 | pubmed:issnType | Print | lld:pubmed |
pubmed-article:12142780 | pubmed:volume | 24 | lld:pubmed |
pubmed-article:12142780 | pubmed:owner | NLM | lld:pubmed |
pubmed-article:12142780 | pubmed:authorsComplete | Y | lld:pubmed |
pubmed-article:12142780 | pubmed:pagination | 337-42 | lld:pubmed |
pubmed-article:12142780 | pubmed:dateRevised | 2011-10-6 | lld:pubmed |
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pubmed-article:12142780 | pubmed:articleTitle | Atypical teratoid/rhabdoid tumor of the central nervous system: report on workshop. | lld:pubmed |
pubmed-article:12142780 | pubmed:affiliation | Department of Neurology, Children's National Medical Center, The George Washington University Medical Center, Washington, DC 20010, USA. rpacker@cnmc.org | lld:pubmed |
pubmed-article:12142780 | pubmed:publicationType | Research Support, U.S. Gov't, P.H.S. | lld:pubmed |
pubmed-article:12142780 | pubmed:publicationType | Congresses | lld:pubmed |
pubmed-article:12142780 | pubmed:publicationType | Research Support, Non-U.S. Gov't | lld:pubmed |
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