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pubmed-article:11229634pubmed:abstractTextThe association between Tuberous Sclerosis (TS) and Angiomyolipoma (AML) is well known. A patient with TS and giant AML mimicking Renal Cell Carcinoma (RCC), measuring 29 x 18 x 11 cm, weighing 4700 gr is presented. Imaging studies revealed coexistent pulmonary lymphangioleiomyomatosis and concurrent renal and pulmonary involvement is extremely rare in patients in TS. We believe that the growth potential of this hamartomatous lesion may reach to a life threatening size.lld:pubmed
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pubmed-article:11229634pubmed:volume32lld:pubmed
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pubmed-article:11229634pubmed:pagination219-22lld:pubmed
pubmed-article:11229634pubmed:dateRevised2005-11-17lld:pubmed
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pubmed-article:11229634pubmed:articleTitleGiant angiomyolipoma associated with marked pulmonary lesions suggesting lymphangioleiomyomatosis in a patient with tuberous sclerosis.lld:pubmed
pubmed-article:11229634pubmed:affiliationDokuz Eylül University, School of Medicine, Department of Urology, Inciralti, Izmir, Turkey.lld:pubmed
pubmed-article:11229634pubmed:publicationTypeJournal Articlelld:pubmed
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